The topic Massive Diffuse Soft Tissue Plexiform Neurofibroma you are seeking is a synonym, or alternative name, or is closely related to the medical condition Elephantiasis Neuromatosa.

Quick Summary:

• Elephantiasis Neuromatosa is an advanced form of plexiform neurofibroma, in which the entire extremity (arm or leg) is involved. It results in massive hypertrophy (enlargement) of the affected skin, underlying soft tissue, and bone structure
• Plexiform neurofibroma is an uncommon form of neurofibroma that is slow-growing and asymptomatic. A majority of these tumors are benign. A neurofibroma is a type of peripheral nerve sheath tumor (PNST)
• Study reports indicate that plexiform neurofibroma, and consequently Elephantiasis Neuromatosa, is unique to those with neurofibromatosis type 1 (NF-1), which is a genetic disorder
• Elephantiasis Neuromatosa can result in severely impaired function of the affected region, severe physical disfigurement, and emotional stress. The individual is also vulnerable to bone fractures due to weakening of the affected bones
• The mainstay of treatment of Elephantiasis Neuromatosa involves surgery, which is mainly undertaken to address cosmetic issues. In many cases, more than one surgical procedure is required
• The prognosis of Elephantiasis Neuromatosa depends on the site of involvement and success of surgery. In a majority, complete restoration of the affected area may not be possible

Please find comprehensive information on Elephantiasis Neuromatosa regarding definition, distribution, risk factors, causes, signs & symptoms, diagnosis, complications, treatment, prevention, prognosis, and additional useful information HERE.