The topic Localized Fibrosing Disorder due to Linear Scleroderma you are seeking is a synonym, or alternative name, or is closely related to the medical condition Localized Linear Scleroderma.

Quick Summary:

• Localized Linear Scleroderma is a condition typically found on the limb or face of a child or young adult; it can affect one or both limbs
• Scleroderma is a chronic connective tissue disorder of unknown cause. Connective tissues give support to the organs and skin. Individuals with Scleroderma have thick or hard connective tissue

• There is currently a debate about how Scleroderma should be classified. A majority believe that it should be classified as an autoimmune rheumatologic disorder. Due to this, many researchers believe that the damage is caused by immune cells mistakenly attacking one’s own healthy tissue.

  Scleroderma can be classified into 2 broad categories, which include Localized Scleroderma and Systemic Scleroderma:

  • Localized Scleroderma:
    • It often affects the skin tissues and does not cause harm to the other major organs
    • There are two types of Localized Scleroderma, namely Morphea and Localized Linear Scleroderma
  • Systemic Scleroderma:
    • It affects the skin, tissue beneath the skin, major organs, and blood vessels
    • Systemic Scleroderma also has 2 different types, namely Limited Systemic Scleroderma and Diffuse Systemic Scleroderma

• Localized Linear Scleroderma is a type of Localized Scleroderma of unknown cause.

  • In this disorder, a hardened line of skin can occur in any part of the body; however, the more common areas include the arms, legs, and forehead. When this hardened line occurs on the face it  is called “en coup de sabre”. This term reflects the appearance of the lesion to an old-healed blow from a saber. The signs and symptoms do not progress in a rapid manner and can vary greatly from individual to individual
  • The complications of Localized Linear Scleroderma include tightening of facial skin to a great degree causing the nearby functional areas, such as the mouth, to become narrower and smaller or restriction of movement of a limb
  • There is currently no cure for Localized Linear Scleroderma, but medications and therapy may be used to control symptoms and prevent complications
• The prognosis of Localized Linear Scleroderma is usually excellent, as it is a localized form of Scleroderma. Individuals with this form of Scleroderma do not present the involvement of other organs, other than skin

Please find comprehensive information on Localized Linear Scleroderma regarding definition, distribution, risk factors, causes, signs & symptoms, diagnosis, complications, treatment, prevention, prognosis, and additional useful information HERE.