The topic Arteriohepatic Dysplasia (AHD) you are seeking is a synonym, or alternative name, or is closely related to the medical condition Alagille Syndrome.

Quick Summary:

• Alagille Syndrome is a genetic condition that affects the heart, liver, and several other important organs of the body. It is a multisystem disorder that affects many body organs. The disorder is seen among neonates with equal incidence between males and females
• In Alagille Syndrome, there is malformation of the bile ducts within the liver; these ducts are either narrowed, abnormally formed, or reduced in number
• These small ducts within the liver are responsible for transporting bile from the cells in the liver to the gallbladder that eventually makes its way into the small intestine
• The bile within the liver is important for two reasons - to remove harmful toxins and wastes out of the body and to help in the digestion of fatty material
• Unfortunately, because there is minimal availability of bile ducts in Alagille Syndrome, it causes an obstruction in the flow of bile, leading to a back-up of all the material that is not transported out of the liver. This eventually leads to liver damage and scarring
• Currently there is no treatment available for Alagille Syndrome. It has a poor prognosis, as there are currently no known effective treatment options to manage this genetic condition. It cannot be prevented too, since the condition is inherited

Please find comprehensive information on Alagille Syndrome regarding definition, distribution, risk factors, causes, signs & symptoms, diagnosis, complications, treatment, prevention, prognosis, and additional useful information HERE.