The topic Chordoepithelioma you are seeking is a synonym, or alternative name, or is closely related to the medical condition Chordoma.

Quick Summary:

• A Chordoma is a rare, slow-growing, malignant tumor. The tumor arises from cells called the ‘notochordal remnants’, situated at the sides of the vertebral column. Notochord is the embryonic structure from which the brain and spinal cord develop, during fetal development
• Chordomas comprise less than 1% of central nervous system (CNS) tumors. They are commonly observed in 3 locations:
  • 50% of them are reported in the sacrococcygeal region (bottom of the spine)
  • The next common site is the brainstem (the posterior part, where the spinal cord joins the cerebrum/brain)
  • The least common site is the spinal axis cervical region
  • Rarely, Chordomas may also occur in extra-axial locations (away from the vertebral column midline)
• Individuals with a positive family history of this condition have a higher risk of developing these malignant tumors, later in one’s life
• Generally, mid-to-elderly adults are seen with this infrequent CNS tumor. Depending on the location of these slow-growing tumors, they can cause local bone destruction and extend deep into the soft tissues
• The treatment of choice for Chordoma that affects the brain and central nervous system is a complete surgical removal of the tumor, which reduces the risk of recurrence
• The prognosis depends on many factors, such as the individual’s age, site and size of the tumor; though largely, the prognosis of Chordoma is poor

Please find comprehensive information on Chordoma regarding definition, distribution, risk factors, causes, signs & symptoms, diagnosis, complications, treatment, prevention, prognosis, and additional useful information HERE.